Printable factfile
CINCA syndrome is a rare congenital inflammatory disorder characterized by a triad of neonatal onset of cutaneous symptoms, chronic meningitis, and joint manifestations with recurrent fever and inflammation.
Alternative names
FCAS, CINCA, NOMID
Multisystem inflammatory disease, neonatal-onset
Neonatal onset multisystem inflammatory disease
Chronic infantile neurologic cutaneous articular syndrome
Classification
- Periodic fever syndromes
- Cold autoinflammatory syndrome
Inheritance
Autosomal dominant
Cross references
Phenotypically related immunodeficiencies
IDR factfile for Familial cold urticaria and Muckle-Wells syndrome
IDR factfile for Granulomatous sinovitis with uveitis and cranial neuropathies
Incidence
Incidence is not known.