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Patients have an increased susceptibility to infections. Neisserial infections have been reported in half of the cases. Due to defective opsonization, patients are susceptible to recurrent pyogenic infections. Some patients also can be asymptomatic. Rheumatic disorder are not common.
Diagnosis
Diagnostic recommendations
Additional Information
Therapeutic options
- Fresh frozen plasma is used for emergent replacement of complements components. Supportive therapy is used for complement deficiencies.
- Complement deficiency, eMedicine
- Complement deficiency, eMedicine